[Epithelioid angiosarcoma of the adrenal gland. Report of a case].

OBJECTIVES We report one case of adrenal epithelioid angiosarcoma. METHODS We review the clinical and histopathological features of this rare adrenal sarcoma and perform a bibliographic review. RESULTS A 60 year old male without past medical history presented with a six week flank pain. CT scan and MRI showed a big adrenal tumor without renal involvement. Definitive diagnosis was obtained by histopathological study and immunohistochemical techniques. CONCLUSIONS Although adrenal sarcomas are rare, angiosarcoma must be considered in the differential diagnosis of every adrenal tumor. Surgery is the treatment of choice with or without adjuvant chemotherapy/radiotherapy, depending on pathological stage and prognostic factors derived from the histopathological study.